Ukudla kwe-PKU kuyadingeka kubantu abanesifo sofuzo okuthiwa phenylketonuria (PKU). Abantu abane-phenylketonuria abanakho i-enzyme evumela umzimba ukuba uguqule i-phenylalanine (i-amino acid) ku-tyrosine (enye i- amino acid ). I-phenylalanine yakha futhi ibangela ukulimala kwengqondo; ngakho wonke umuntu ophethe i-PKU kumele agweme ukudla okunamaprotheni.
Izinsana nezinsana ezinePKU zidinga ifomula ekhethekile engenayo i-phenylalanine.
Kubaluleke kakhulu ukuthi izingane, izingane ezincane, nezingane azidle ukudla okunamaprotheni ngoba ubuchopho bukhula ngokushesha. Ukudla okunzima kakhulu kufanele kulandelwe. Zonke ukudla eziphezulu amaprotheni kudingeka zigweme.
Ukudla okuphezulu amaprotheni kufaka:
- inyama
- inhlanzi
- izinkukhu
- ubisi
- i-yogurt
- ushizi
- amaqanda
- amantongomane
- imbewu
- i-legumes
- i-peanut nezinye ibhotela
Izitsha zokudla, ukudla okulula, kanye nokudla okwenziwa nalezi zokudla kudingeka futhi kugwenywe - ngakho-ke i-pizza, ikhekhe, amakhukhi, ama-hamburgers, izinja ezishisayo, i-ayisikhilimu, i-yogurt nokunye okunye ukudla. Ngisho nezinto ezifana nesinkwa kanye neminye imikhiqizo ye-cereal ingaba namaprotheni amaningi kakhulu. I-Aspartame nayo idinga ukugwema ngoba inhlanganisela ye-aspartic acid ne-phenylalanine.
Izingane kanye nentsha ephethe i-PKU ingadla izithelo nemifino kanye namanani amancane okusanhlamvu kanye nabaqaphi ngoba lezo zokudla ziphansi amaprotheni. Abantu abadala badinga ukunamathela eduze kokudla.
Kodwa, ukudla kwe-PKU kuncane kakhulu kumaprotheni for impilo evamile, ngakho izingane kanye nabantu abadala abane-PKU kudingeka badle iziphuzo ezikhethekile zeprotheni ezakhiwe ngaphandle kwe-phenylalanine.
Futhi, lokhu kudla kudinga ukulandelwa impilo, futhi ukuhlolwa kwegazi kuthathwa njalo ukugcina ithrekhi yamazinga e-phenylalanine emzimbeni.
Ingabe i-PKU evamile?
Ngokusho kwe-National PKU Alliance, cishe ingane eyodwa kwabangu-15 000 inamaphutha. Izingane zase-United States nakwamanye amazwe amaningi zihlolwe ngokushesha ngemva kokuzalwa, futhi uma nje abantwana nezingane behambisana nokudla, ubuchopho babo buyokhula ngendlela evamile.
Abantu abadala abane-PKU bangase babe ne-leeway encane nge-protein yokudla ngenxa yokuthi ubuchopho buyathuthuka ngokugcwele, kodwa i-PKU ayishiyi futhi idla i-phenylalanine kakhulu ingabangela izinkinga zemizwelo nokulahleka kwememori.
Imithombo:
Maher AK. "Imenyu Yokudla Elula." I-Eleventh Edition, eHoboken NJ, eU.SA: Wiley-Blackwell Publishing, ngo-Okthoba 2011.
I-Merck Manual - Professional Version. "I-Amino Acid ne-Organic Acid Metabolism Disorders." http://www.merckmanuals.com/professional/pediatrics/inherited-disorders-of-metabolism/overview-of-amino-acid-and-organic-acid-metabolism-disorders.
I-National Phenylketonuria Alliance. "I-Phenylketonuria Imininingwane yeSikole Sokuqeqeshelwa Isikole nabasebenzi." http://www.npkua.org/Portals/0/PKU_schoolfacts.pdf .